perivascular epithelioid cell tumor (PAYR-ee-VAS-kyoo-ler eh-pih-THEE-lee-oyd sel TOO-mer)
A family of rare tumors that form in the soft tissues of the stomach, intestines, lungs, female reproductive organs, and genitourinary organs. Most perivascular epithelioid cell tumors are benign (not cancer). They often occur in children with an inherited condition called tuberous sclerosis. Also called PEComa.