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Wilms Tumor and Other Childhood Kidney Tumors Treatment (PDQ®)

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Multilocular Cystic Nephroma

General Information About Multilocular Cystic Nephroma

Multilocular cystic nephromas are benign lesions consisting of cysts lined by renal epithelium. These lesions can occur bilaterally, and a familial pattern has been reported.

Multilocular cystic nephroma has been associated with pleuropulmonary blastomas, so radiographic imaging studies of the chest are monitored in patients with multilocular cystic nephroma.[1] (Refer to the Clinical Features and Diagnostic and Staging Evaluation sections of this summary for more information about the clinical features and diagnostic evaluation of childhood kidney tumors.)

Standard Treatment Options for Multilocular Cystic Nephroma

The standard treatment for multilocular cystic nephroma is surgery.


  1. Ashley RA, Reinberg YE: Familial multilocular cystic nephroma: a variant of a unique renal neoplasm. Urology 70 (1): 179.e9-10, 2007. [PUBMED Abstract]
  • Updated: August 15, 2014