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Wilms Tumor and Other Childhood Kidney Tumors Treatment (PDQ®)

Health Professional Version
Last Modified: 06/27/2014

Desmoplastic Small Round Cell Tumor of the Kidney

Desmoplastic small round cell tumor of the kidney is a rare, small, round blue tumor of the kidney. It is diagnosed by its characteristic EWS-WT1 translocation.[1] (Refer to the Desmoplastic small round cell tumor section in the PDQ summary on Childhood Soft Tissue Sarcoma Treatment for more information about desmoplastic small round cell tumor of the kidney.)

References
  1. Wang LL, Perlman EJ, Vujanic GM, et al.: Desmoplastic small round cell tumor of the kidney in childhood. Am J Surg Pathol 31 (4): 576-84, 2007.  [PUBMED Abstract]