NCI Dictionary of Cancer Terms
The NCI Dictionary of Cancer Terms features 8,357 terms related to cancer and medicine.
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- Kostmann neutropenia
- listen (KOST-mun noo-troh-PEE-nee-uh)
An inherited disorder in which there is a lower-than-normal number of neutrophils (a type of white blood cell that is important in fighting infections). Infants with the disorder get infections caused by bacteria, and are at an increased risk of acute myelogenous leukemia (AML) or myelodysplasia (a bone marrow disorder). Also called congenital neutropenia, genetic infantile agranulocytosis, infantile genetic agranulocytosis, Kostmann disease, and Kostmann syndrome.